a. Being of Mediterranean descent put my child at risk for the disease.
b. My child will need lifelong treatment but will have a normal lifespan.
c. My child will be anemic but won’t have symptoms that require treatment.
d. The problem is too few red blood cells are made and some get destroyed.
146. Which statement made by a client with sickle cell anemia indicates a correct understanding of an aspect of the disease?
a. I inherited my disease from my father and his side of the family
b. Any children I have will also have the disease.
c. If I had my spleen removed, my symptoms would basically disappear.
d. My red blood cells only sickle when oxygen tension in my blood decreases.
145. Correct answer: b.
Thalassemia minor is generally asymptomatic and does not require treatment. It is an inherited disorder which most often affects persons of Mediterranean descent. The disease is characterized by decreased production of RBCs and chronic hemolytic anemia.
146. Correct answer: d.
The hemoglobin S red blood cell, which has normal oxygen-carrying capacity, forms a sickle shape under conditions of decreased oxygen tension in the blood. The sickled cells tend to clump and block small blood vessels thereby causing tissue hypoxia. Sickle cell anemia is inherited as an autosomal recessive disorder which means a defective gene had to be inherited from both the mother and the father. Therefore, if a woman with sickle cell anemia has a child with a man who does not have the disease and is not a carrier; the child will be a carrier but will not have the disease itself. Splenectomy does not relieve the symptoms of sickle cell disease; it relieves the symptoms of hereditary spherocytosis.